Cystic Fibrosis

cdunbar4's version from 2016-10-10 00:08


Question Answer
Descriptionautosomal recessive; altered exocrine gland function
Organs it involves?Lungs, pancreas and sweat glands
Characterized by: abnormal, thick, abundant secretions. Leads to a chronic diffuse obstruction pulmonary disorder.
1st sign of CF (adult)cough (becomes productive with purulent green mucous)
Symptoms that are increasingly occuring, with periods of stabilizationrecurring lung infections
Symptoms can also include (r/t abdomen)RLQ pain, N/V, anorexia
Diagnosis bysweat chloride test
Collaborative care includespromote secretion; control infection; provide adequate nutrition
Nursing managmentrelief of respiratory sx; chest pt; antibiotics; o2 tx; steroids; psyho-social support; family support; agency referral d/t lifetime financial burden
Sx in newborn that may be initial sign of CFmeconium ileus (obstruction of bowel caused by thick, abnormal meconium)
Other Sx's in newbornsfailure to grow, clubbing of fingers, persistent cough with mucous production; tachypnea; large, frequent BM

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